Accessory mitral valve tissue causing severe left ventricular outflow tract obstruction in a post-Senning patient with transposition of the great arteries

Background: Patients with adult congenital heart disease (ACHD) are more prone to atrial arrhythmia, which increases their morbidity and mortality and risk of hospital admissions when compared with the same population where atrial arrhythmias are absent. Objective: Compare the use ...

First described in 1868 by WS Church, cor triatriatum sinister (CTS) is one of the rarest congenital heart diseases in the world, with an estimated incidence of 0.1%.1,2 It is characterised by the presence of a fibrous membrane that divides the left ...

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Short QT syndrome (SQTS) is a cardiac channelopathy characterised by an abnormally short QT interval and an increased risk of atrial and ventricular fibrillation.1 As it often involves young patients with an apparently normal heart, it is imperative for physicians ...

Long QT syndrome (LQTS) is a hereditary disorder characterised by prolongation of the QT interval on electrocardiogram (ECG), syncope and sudden death due to torsade de pointes (Tdp) and/ or ventricular fibrillation.1 To date, 16 genes have been reported as LQTS-causing ...

Advances in surgical technique over the last two decades have heralded a dramatic improvement in survival rates in those born with congenital heart disease (CHD). With current methods, more than 85% of paediatric patients undergoing surgical repair survive into adulthood,1and ...

Brugada syndrome (BrS), first described in 1992, is an autosomal dominant, arrhythmogenic disease. There is a male predominance of the syndrome and the prevalence is highest in Asian and Southeast Asian countries, reaching 0.5.1 per 1,000.1 BrS is diagnosed in patients with ST-segment ...